rpcardioRational Pharmacotherapy in CardiologyРациональная Фармакотерапия в Кардиологии1819-64462225-3653«SILICEA-POLIGRAF» LLC10.20996/1819-6446-2015-11-6-638-642rpcardio-445Research ArticlePOINT OF VIEWТОЧКА ЗРЕНИЯThe non-compact left ventricle cardiomyopathy: clinical features and diagnostic capabilitiesНЕКОМПАКТНАЯ КАРДИОМИОПАТИЯ ЛЕВОГО ЖЕЛУДОЧКА: ОСОБЕННОСТИ КЛИНИЧЕСКОГО ТЕЧЕНИЯ И ВОЗМОЖНОСТИ ДИАГНОСТИКИМершинаЕ. А.MershinaE. A.

к.м.н., зав. отделением томографии ЛРЦ; доцент кафедры лучевой диагностики, лучевой терапии и медицинской физики РМАПО

МясниковР. П.MyasnikovR. P.

к.м.н., н.с. отдела клинической кардиологии и молекулярной генетики ГНИЦ ПМ

RMyasnikov@gnicpm.ruКуликоваО. В.KulikovaO. V.

врач-кардиолог ГНИЦ ПМ

ХарлапМ. С.KharlapM. S.

к.м.н., с.н.с. отдела клинической кардиологии и молекулярной генетики ГНИЦ ПМ

КорецкийС. Н.KoretskiyS. N.

к.м.н., врач функциональной диагностики ГНИЦ ПМ

ЛаринаО. М.LarinaO. M.

к.м.н., врач-рентгенолог отделения томографии ЛРЦ

СиницынВ. Е.SinitsynV. E.

д.м.н., профессор, руководитель Центра лучевой диагностики ЛРЦ; профессор кафедры лучевой диагностики, лучевой терапии и медицинской физики РМАПО

БойцовС. А.BoytsovS. A.

д.м.н., профессор, директор ГНИЦ ПМ

Лечебно-реабилитационный центр. 125367, Москва, Иваньковское шоссе, 3 Российская медицинская академия последипломного образования 123995, Москва, ул. Баррикадная, 2/1РоссияTreatment and Rehabilitation Center. Ivankovskoe shosse 3, Moscow, 125367 Russia Russian Medical Academy of Postgraduate Education. Barricadnaya ul. 2/1, Moscow, 123995 RussiaRussian FederationГосударственный научно-исследовательский центр профилактической медицины 101000, Москва, Петроверигский пер., 10РоссияState Research Centre for Preventive Medicine. Petroverigsky per. 10, Moscow, 101990 RussiaRussian FederationЛечебно-реабилитационный центр. 125367, Москва, Иваньковское шоссе, 3РоссияTreatment and Rehabilitation Center. Ivankovskoe shosse 3, Moscow, 125367 RussiaRussian Federation201530122015116638642Copyright © Mershina E.A., Myasnikov R.P., Kulikova O.V., Kharlap M.S., Koretskiy S.N., Larina O.M., Sinitsyn V.E., Boytsov S.A., 20152015Мершина Е.А., Мясников Р.П., Куликова О.В., Харлап М.С., Корецкий С.Н., Ларина О.М., Синицын В.Е., Бойцов С.А.Mershina E.A., Myasnikov R.P., Kulikova O.V., Kharlap M.S., Koretskiy S.N., Larina O.M., Sinitsyn V.E., Boytsov S.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.rpcardio.online/jour/article/view/445

The non-compact left ventricular cardiomyopathy (NCLVC) refers to the non-classified cardiomyopathies. Its cause is not completely clear. NCLVC is characterized by an increased trabecular with the formation of deep intertrabecular crypts. It can exist either in isolated form or in combination with other congenital diseases. The clinical features of NCLVC are different: asymptomatic forms are identified as well as forms with the progressive course of the disease, with heart failure, angina, thromboembolic complications, and ventricular arrhythmias. In some cases, the disease starts with the sudden cardiac death. The sudden decompensation of NCLVC also could arise due to the development of acute myocarditis

Некомпактная кардиомиопатия левого желудочка (НКМЛЖ) относится к неклассифицируемым кардиомиопатиям, генез её до конца не ясен. Данный вид кардиомиопатии характеризуется повышенной трабекулярностью с образованием глубоких межтрабекулярных карманов. НКМЛЖ может существовать как в виде изолированной формы, так и в сочетании с другими врожденными заболеваниями. Клиническая картина кардиомиопатии различна: выявляются как бессимптомные формы, так и формы с прогрессивным течением заболевания, проявляющимся сердечной недостаточностью, стенокардией, тромбоэмболическими осложнениями, желудочковыми злокачественными нарушениями ритма сердца. В некоторых случаях болезнь дебютирует с развития внезапной сердечной смерти. В то же время существует проблема внезапной декомпенсации НКМЛЖ, существенный вклад в развитие которой вносит присоединение острого миокардита.

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The authors declare that there are no conflicts of interest present.