rpcardioRational Pharmacotherapy in CardiologyРациональная Фармакотерапия в Кардиологии1819-64462225-3653«SILICEA-POLIGRAF» LLC10.20996/1819-6446-2009-5-2-65-69rpcardio-635Research ArticleASSOCIATED PROBLEMS OF CARDIOLOGYСМЕЖНЫЕ ПРОБЛЕМЫ КАРДИОЛОГИИSECONDARY PULMONARY ARTERIAL HYPERTENSION IN SYSTEMIC DISEASES OF CONNECTIVE TISSUEВТОРИЧНАЯ ЛЕГОЧНАЯ АРТЕРИАЛЬНАЯ ГИПЕРТЕНЗИЯ ПРИ СИСТЕМНЫХ ЗАБОЛЕВАНИЯХ СОЕДИНИТЕЛЬНОЙ ТКАНИШостакН. А.ShostakN. A.

Кафедра факультетской терапии им. акад. А.И. Нестерова 

117997 Москва, ул. Островитянова, 1

Chair of Faculty Therapy named after academician A.I. Nesterov

НовиковЮ. К.NovikovJ. K.

Кафедра пульмонологии 

117997 Москва, ул. Островитянова, 1

Chair of Pulmonology

ЧерняевА. Л.ChernayevA. L.

Кафедра пульмонологии 

117997 Москва, ул. Островитянова, 1

Chair of Pulmonology

КлименкоА. А.KlimenkoA. A.

Кафедра факультетской терапии им. акад. А.И. Нестерова 

117997 Москва, ул. Островитянова, 1

Chair of Faculty Therapy named after academician A.I. Nesterov

НовиковП. В.NovikovP. V.

Кафедра факультетской терапии им. акад. А.И. Нестерова 

117997 Москва, ул. Островитянова, 1

Chair of Faculty Therapy named after academician A.I. Nesterov

sobstvennost@rambler.ruРоссийский государственный медицинский университет РосздраваРоссияRussian State Medical UniversityRussian Federation200909012016526569Copyright © Shostak N.A., Novikov J.K., Chernayev A.L., Klimenko A.A., Novikov P.V., 20162016Шостак Н.А., Новиков Ю.К., Черняев А.Л., Клименко А.А., Новиков П.В.Shostak N.A., Novikov J.K., Chernayev A.L., Klimenko A.A., Novikov P.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.rpcardio.online/jour/article/view/635

Modern definition of pulmonary arterial hypertension (PAH) as well as data on prevalence and incidence of secondary PAH in systemic disease of connective tissue is presented,  including data of USA, France and Scotland registers. The main chains of pathogenesis, classification approaches, clinical features and diagnostics are described. 

Приводятся современное определение легочной артериальной гипертензии (ЛАГ), данные о распространенности и встречаемости вторичной ЛАГ при системных заболеваниях соединительной ткани (СЗСТ), в том числе на основе регистров США, Франции и Шотландии. Описаны основные звенья патогенеза, классификационный подход, клиника и этапы диагностики.

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The authors declare that there are no conflicts of interest present.