CYSTIC MEDIONECROSIS OF PULMONARY ARTERIAL TRUNK AS A PROBABLE CAUSE OF THROMBOSIS OF ITS BRANCHES
https://doi.org/10.20996/1819-6446-2017-13-6-806-812
Abstract
The article presents a rare clinical case of thrombosis of large and small branches of the pulmonary artery, the probable cause of which was the degeneration of the muscle fibers of the wall of the pulmonary artery trunk by type of the cystic medionecrosis, possibly having a viral etiology. The disease was associated with the tumor of the pancreas body, smoldering purulent pancreatitis complicated by the syndrome of disseminated intravascular coagulation.
About the Authors
S. А. BolduevaRussian Federation
Svetlana A. Boldueva – MD, PhD, Professor, Chair of Faculty Therapy
Kirillovskaya ul. 14, St. Petersburg, 191015
V. B. Petrova
Russian Federation
Victoria B. Petrova – MD, PhD, Cardiologist, Department of Сardiosurgery with Surgical Treatment of Complex Heart Rhythm Disorders
Kirillovskaya ul. 14, St. Petersburg, 191015
I. A. Danilova
Russian Federation
Irina A. Danilova – MD, PhD, Professor, Chair of Pathological Anatomy
Kirillovskaya ul. 14, St. Petersburg, 191015
References
1. Dermengiu S., Ceausu M., Hostiuc S., et al. Spontaneous aortic dissection due to cystic medial degeneration. Report of a sudden death case and literature review. Rom J Leg Med. 2009;17(2):89-96. doi: 10.4323/rjlm.2009.89
2. Schievink W.I., Parisi J.E., Piepgras D.G., Michels V.V. Intracranial aneurysms in Marfan syndrome: an autopsy study. Neurosurgery. 1997;41:866-870. doi:10.1097/00006123-199710000-00019
3. Crivello M.S., Porter D.H., Kim D., et al. Isolated external iliac artery aneurysm secondary to cystic medial necrosis. Cardiovasc Intervent Radiol. 1986;9(3):139-41. doi: 10.1007/BF02577923
4. Fee H.J., Gewirtz H.S., O’Connell T.X., Grollman J.H. Bilateral subclavian artery aneurysm associated with idiopathic cystic medial necrosis. Ann Thorac Surg. 1978;26(4):387-90. doi: 10.1016/S00034975(10)62908-6
5. Marsalese D.L., Moodie D.S., Lytle B.W., et al. Cystic medial necrosis of the aorta in patients with Marfan's syndrome: surgical outcome and long-term follow-up. J Am Coll Cardiol. 1990;16(1):68-73. doi: 10.1016/0735-1097(90)90458-2
6. Gsell O. Wandnekrosen der Aorta als selbstКndige Erkrankung und ihre Beziehung zur Spontanruptur. Virchows Arch F Path Anat. 1928;270:1.1-36. doi: 10.1007/BF01892241
7. Erdheim J.Medionecrosis aortae idiopathica. Virchows Arch F Path Anat. 1929;273:454-79. doi: 10.1007/BF02158989
8. Hirst A.E., Gore I. Is cystic medionecrosis the cause of dissecting aortic aneurysm? Circulation. 1976;53(6):915-6. doi: 10.1161/01.CIR.53.6.915
9. Yuan S.M., Jing H. Cystic medial necrosis: pathological findings and clinical implications. Rev Bras Cir Cardiovasc. 2011;26:107-15. doi: 10.1590/S0102-76382011000100019
10. Rawson A.J. Incomplete rupture of the pulmonary artery based on cystic medionecrosis. Am Heart J. 1958;55(5):766-71. doi:10.1016/0002-8703(58)90017-6
11. Levy H. Partial rupture of pulmonary artery with lesions of medionecrosis in a case of mitral stenosis. Am Heart J. 1961;62:31-42. doi:10.1016/0002-8703(61)90483-5.
12. Natelson E.A., Watts H.D., Fred H.L. Cystic medionecrosis of the pulmonary arteries. Chest. 1970 Apr;57(4):333-5. doi: 10.1378/chest.57.4.333
Review
For citations:
Boldueva S.А., Petrova V.B., Danilova I.A. CYSTIC MEDIONECROSIS OF PULMONARY ARTERIAL TRUNK AS A PROBABLE CAUSE OF THROMBOSIS OF ITS BRANCHES. Rational Pharmacotherapy in Cardiology. 2017;13(6):806-812. (In Russ.) https://doi.org/10.20996/1819-6446-2017-13-6-806-812